Low-complexity domain of U1-70K modulates phase separation and aggregation through distinctive basic-acidic motif

March 24, 2020

Title

Low-complexity domain of U1-70K modulates phase separation and aggregation through distinctive basic-acidic motif

Author

Song Xue, Rui Gong, Fanqi He, Yanqin Li, Yunjia Wang, Tianwei Tan, Shi-Zhong Luo

Year

2019

Journal

Science Advances

Abstract

Liquid-liquid phase separation (LLPS) facilitates the formation of functional membraneless organelles and recent reports have linked this phenomenon to protein aggregation in neurodegenerative diseases. Understanding the mechanism of LLPS and its regulation thus promises to shed light on the pathogenesis of these conditions. The RNA-binding protein U1-70K, which aggregates in brains of Alzheimer’s disease patients, is considered a potential target for Alzheimer’s therapy. Here, we report that two fragments in the low-complexity (LC) domain of U1-70K can undergo LLPS. We have demonstrated that the repetitive basic-acidic motifs in these fragments induce nucleotide-independent phase separation and initiate aggregation in vitro. We also have confirmed that LLPS and aggregation occur in vivo and that the content of ampholytic motifs in a protein domain determines the transition between droplets and aggregation, providing insights into the mechanism underlying the formation of diverse assembly states.

Instrument

J-810

Keywords

Circular dichroism, Secondary structure, Biochemistry